Rhabdomyosarcoma

RMS is a neoplasia, occurring in muscular, skeletal tissue. It is very common in infancy (representing 60% of infant sarcomas) and rare in adults. It often occurs in the maxillo-facial area (35% of cases). The tumour presents as a painless, infiltrating and quickly growing mass. The most frequent intra-oral site is the palate. Treatment is with surgery, followed by post-operative chemotherapy and radiotherapy. The survival rate at 5 years varies between 50% and 60% on the basis of histological variants.